Atypical Henoch-Schonlein purpura: a forerunner of familial Mediterranean fever.
نویسندگان
چکیده
Insuception is the most common cause of intestinal obstruction in early childhood. The cause of most intussusceptions is unknown but it can complicate the course of Henoch-Schonlein purpura (HSP) as a result of the vasculitic process. Familial Mediterranean fever (FMF), a common disease in Israel, is also associated with HSP. In a few patients, particularly in children, HSP has been reported to precede the diagnosis of FMF. We describe two patients with an unusual clinical course of severe abdominal pain as a result of intusucception. The correlation between intusucception, HSP and FMF are discussed.
منابع مشابه
Sacroiliitis and Polyarteritis Nodosa in a Patient with Familial Mediterranean Fever.
Familial Mediterranean fever (FMF) is an autoinflammatory disorder with autosomal recessive inheritance, characterized by recurrent fever and episodes of serositis. The condition is known to be caused by mutations in the MEFV (Mediterranean FeVer) gene, located in the short arm of chromosome 16. While more than 310 sequence variants in the MEFV gene have been described to date, the diagnosis is...
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عنوان ژورنال:
- The Israel Medical Association journal : IMAJ
دوره 13 4 شماره
صفحات -
تاریخ انتشار 2011